Objective To explore the feasibility of assessments of functional and environmental factors in children with Duchenne muscular dystrophy (DMD) under the frame of International Classification of Functioning, Disability and Health-Children and Youth Version (ICF-CY). To execute family intervention and to evaluate its effects. Methods A 6-year-and-5-month-old boy with DMD was enrolled to the study. Functional and environmental factors were assessed with the North Star Ambulatory Assessment (NSAA), time tests, hand-held dynamometry assessment, body mass index and family interview. Plans of family intervention were settled and executed for one year and at the end of intervention, the boy received all the above assessments to compare the effects of intervention. Results After one-year family intervention, the muscle strength was improved or maintained in most muscles except abductors of hip and the body mass index did not change. For the activities, the scores of NSAA increased and maintained, and the result of time tests improved. Otherwise, attitude and execution of parents were improved. Conclusion It is feasible to execute family intervention under the frame of ICF-CY in children with DMD. Both children and their family may benefit from the intervention.
LI Hui
,
SHI Wei
,
SU Yi
,
LI Xi-hua
,
LU Kai
,
ZHOU Shui-zhen
,
WANG Yi
. Application of ICF-CY in Family Rehabilitation of Children with Duchenne Muscular Dystrophy[J]. Chinese Journal of Rehabilitation Theory and Practice, 2017
, 23(2)
: 139
-145
.
DOI: 10.3969/j.issn.1006-9771.2017.02.005
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